YMJ. 2012; 6(21): 502-505

A RARE BUT TREATABLE CAUSE OF DILATED CARDIOMYOPATHY: ALCAPA

Cenk Eray Yildiz¹, Koksal Binnetoglu², Aybala Tongut¹, Ayfer Acikgoz³, Bulent Koca⁴, Gurkan Cetin^1
1Department of Cardiovascular Surgery, Istanbul University Institute of Cardiology, Istanbul, Turkey
²Department of Pediatric Cardiology, Kocaeli University School of Medicine, Izmit, Turkey
³Department of Anaesthesiology and Reanimation, Istanbul University Institute of Cardiology, Istanbul, Turkey
⁴Department of Pediatric Cardiology, Istanbul University Cerrahpasa Medical Faculty, Istanbul, Turkey

Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital heart disease (CHD) which accounts for 0.023% of all congenital heart diseases. It is asymptomatic in many cases and is mostly diagnosed in the first few months of life. If untreated, the mortality rate in the first year of life will be more than 90%. We report a 6-month-old infant admitted to out clinic because of heart failure. Echocardiography revealed a dilated cardiomyopathy and left main coronary artery originates from pulmonary artery. Diagnosis was confirmed by coronary angiography and treated succesfully by surgical procedure.

Keywords: Anomaous origin of the left coronary artery from the pulmonary artery; cardiac insufficiency; dilated cardiomyopathy;newborn.

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DİLATE KARDİYOMİYOPATİ’NİN NADİR ANCAK TEDAVİ EDİLEBİLİR BİR SEBEBİ: ALCAPA

Cenk Eray Yildiz¹, Koksal Binnetoglu², Aybala Tongut¹, Ayfer Acikgoz³, Bulent Koca⁴, Gurkan Cetin^1
1Department of Cardiovascular Surgery, Istanbul University Institute of Cardiology, Istanbul, Turkey
²Department of Pediatric Cardiology, Kocaeli University School of Medicine, Izmit, Turkey
³Department of Anaesthesiology and Reanimation, Istanbul University Institute of Cardiology, Istanbul, Turkey
⁴Department of Pediatric Cardiology, Istanbul University Cerrahpasa Medical Faculty, Istanbul, Turkey

Pulmoner arter’den köken alan sol koroner arter anomalisi, oldukça nadir görülen (% 0.023) bir konjenital kalp hastalığıdır. Genellikle yaşamın ilk birkaç ayında teşhis edilir, vakaların çoğu asemptomatiktir. Tedavi edilmezse, bir yıl içinde ölüm oranı % 90’dan fazladır. Burada kalp yetersizliği nedeniyle önce dış merkeze başvuran 6 aylık bir bebek rapor edilmiştir. Kliniğimizde yapılan ekokardiyografi’sinde dilate kardiyomiyopati ve sol ana koroner arter’in pulmoner arter’den kaynaklandığı saptanmış, tanı koroner anjiyografi ile teyit edilerek başarılı bir cerrahi tedavi uygulanmıştır.

Anahtar Kelimeler: Dilate kardiyomiyopati; kalp yetersizliği;sol koroner arterin pulmoner arterden çıkış anomalisi; yenidoğan.

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